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Standing Up for a Better Future After SCI

Background/ Purpose:

Many individuals with spinal cord injury (SCI) face barriers to complex rehab technology (CRT), such as limited insurance benefits, high financial costs, residential structural limitations, and identifying a rehabilitation team knowledgeable in CRT. The purpose of this case is to describe how consistent access and use of a standing frame, in addition to other various devices, have each contributed to function, health, and wellness for an individual in the years following SCI.

Case Description:

The patient is a 65-year-old male diagnosed with T8 AIS A (complete) paraplegia resulting from a car accident in 2002 after being hit by a drunk driver. Before his SCI, the patient enjoyed being active, playing hockey, and riding motorcycles. Following his accident, he utilizes a wheelchair for mobility, and his past medical history includes a right ankle fracture in 2017, neurogenic bowel/ bladder, and detethering of his spinal cord in 2007. The patient attended inpatient rehab immediately following his injury, where he was introduced to using a standing device. He continued clinical use of a standing device as he transitioned to outpatient therapy immediately following his injury to improve his standing tolerance. The patient feared atrophy and osteoporosis, and his goal was to maintain his pre-injury fitness. As he navigated through the rehab continuum, it became clear that complex rehab technology would be his gateway to returning to his active and independent lifestyle.

This patient received a standing frame 2.5 years post-injury (2004) and reported that he immediately began standing in it nightly. Due to exceptional insurance coverage, this patient has gained access to many different home devices over the 22 years following his injury. In addition to his standing frame, he has most notably acquired an FES lower extremity cycle, bilateral lower extremity KAFOs, an exoskeleton, and a dynamic all-terrain wheelchair that can stand and climb stairs.

Outcomes:

Because of his access to a regular standing program in his home and community environment for the past 20 years, the patient reports improved flexibility of his lower extremities, reduced chronic pain, decreased spasticity severity, and maintenance of bone health. The patient demonstrated maintenance of his T-score on his bone density DXA scan over five years from 2016 to 2021. Although categorized as osteopenia to mild osteoporosis, which is usual for individuals with SCI, his doctors were pleased with the stability of his lower extremity T-score DXA scan results.

Discussion:

Although it is impossible to definitively attribute improved outcomes to any one device because the patient receives multiple concurrent interventions, the patient reports numerous benefits from using his standing frame consistently for 20 years. He reports that prolonged use of his standing frame alleviates his tone, maintains his flexibility, keeps his bowel program consistent, and allows him to exercise in standing. He stated, “The frame is key to my overall health. It is a lifetime habit.”

Various complex rehab technologies each play an important role in the function, health, and wellness of an individual living with SCI in different situations and environments. This client is an example of how access to a standing frame, exoskeleton, FES bike, and power wheelchair have each separately and independently played a role in function and health for this individual.  This patient has separate goals with the use of each technology. He reports that his standing frame has consistently afforded him opportunities for various hands-free activities while in a prolonged stance without the assistance of a caregiver, maintenance of muscle tone with the FES bike, dynamic movement, and weight bearing using the exoskeleton when a caregiver is present, and independent access to ADLs and IADLs through his power wheelchair. As clinicians work with individuals with SCI, they can serve as advocates for patients to receive various CRT across the lifespan of an individual’s SCI to meet their changing lifestyle needs.

References:

  1. Logan A, Freeman J, Kent B, et al. Functional standing frame programme early after severe sub-acute stroke (SPIRES): a randomized controlled feasibility trial. Pilot and Feasibility Studies 2022; 8:50.
  2. Logan A, Freeman J, Kent B, et al. Standing Practice in Rehabilitation Early after Stroke (SPIRES): a functional standing frame programme (prolonged standing and repeated sit to stand) to improve function and quality of life and reduce neuromuscular impairment in people with severe sub-acute stroke- a protocol for a feasibility randomised controlled trial. Pilot and Feasibility Studies 2018; 4:66.
  3. Paleg G and Livingstone R. Systematic review and clinical recommendations for dosage of supported home-based standing programs for adults with stroke, spinal cord injury and other neurological conditions. BMC Musculoskeletal Disorders 2015; 16: 358.
  4. Valenzuela-Aedo F, Reyes-Moreno C, Balboa- Castillo T. Effectiveness of assisted standing on bone mineral density in children with cerebral palsy. A systematic review. Archivos Argentinos Pediatria 2024; e202310251.
  5. Spinal Cord Injury Centre Physiotherapy Lead Clinicians United Kingdom and Ireland (2013) Clinical guidelines for standing following spinal cord injury.
  6. Newman M and Barker K. The effect of supported standing in adults with upper motor neuron disorders: a systemic review. Clinical Rehabilitation 2012; 26 (12) 1059-1077.
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Greta – Cerebral Palsy – spastic, quadriplegic

Brief description of environment of facility/school

Greta is served through  Early Intervention with a trans-disciplinary, family routines-based model and Physical Therapist as primary service provider.

Basic Info about client

  • Greta
  • Age: 30 months
  • Diagnosis: Cerebral Palsy – spastic, quadriplegic
  • Brief history:
    • born after an uncomplicated pregnancy at 39 3/7 weeks
    • at birth, she had a heart rate of 92 but no spontaneous respirations
    • Apgars were 3 at birth; 4 at one minute; and 4 at ten minutes
    • shortly after birth, Greta had Sarnat stage III encephalopathy and on admission to Newborn Intensive Care Unit at 2 ½ hours of age, she had stage II encephalopathy
    • initial EEG showed occasional electrographic seizures. She was cooled for 72 hours and her EEG showed improvement
    • receives regularly scheduled botulinum toxin injections to most affected areas (usually upper extremity)
    • had trial of Sinemet for motor function, but drug was discontinued due to gastrointestinal side effects (vomiting)

Continue reading Greta – Cerebral Palsy – spastic, quadriplegic

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Eli – Cerebral Palsy

Basic Info about client

Client’s Name: Eli
Age: 2 (will be 3 on 4/2/15)
Diagnosis: Cerebral Palsy
Brief history:
Premature birth – 35 weeks gestation
Sustained intrauterine ischemic event with damage to left parietal lobe, right occipital lobe, Macrodactyly left foot
Current Situation: Eli’s primary means of independent mobility is crawling with a non-reciprocating “bunny hop” pattern. He crawls up and down stairs and pulls to standing independently. He has decreased function of his right upper extremity, but consistently uses his right “helper hand”. Spasticity is present through both legs and right arm. Eli demonstrates typical crouch gait alignment in standing, tending toward bilateral ankle plantarflexion, and flexion at both knees and hips. He propels a gait trainer with minimal assist with forearm prompts and does best with ankle prompts to minimize scissoring and anterior rotation of the left side of the body. He requires verbal prompting to step to or step through with his right foot. Eli has bilateral Ankle Foot Orthotics (AFOs) to assist with alignment of his feet and lower legs. Continue reading Eli – Cerebral Palsy

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Dempsey – Achondroplasia, Cerebral Palsy

Brief description of environment of facility/school

Dempsey is seen by his school district’s Early Intervention team, with visits from the Physical Therapist twice per month as primary service provider with consultation from Early Childhood Special Education teacher and Service Coordinator.

Basic Info about client

Clients Name – Dempsey
Age – 10 months
Diagnosis – achondroplasia, cerebral palsy
Brief history – Dempsey’s mother experienced premature preterm rupture of membranes (PPROM) at 31 weeks, 3 days gestation and was hospitalized. Dempsey was delivered at 34 weeks, 1 day gestation with birth weight of 2400 grams. His Apgar scores were 3 at 1 minute and 8 at 5 minutes. He required positive pressure ventilation with oxygen and had ongoing care in the NICU for respiratory distress syndrome. MRI indicated severe hypoxic ischemic injury, multifocal cerebral, cerebellar, and intraventricular areas of microhemorrhage. Continue reading Dempsey – Achondroplasia, Cerebral Palsy